Interstitial Lung Disease
Goodpasture's Syndrome
Autoantibodies to alveolar basement membrane
= pulmonary Hg & fibrosis
Autoantibodies to glomerular basement membrane
= proliferative, crescentic glomerulonephritis
Ix
serum anti-BM (basement membrane) antibodies
Wegener's Granulomatosis
Systemic vasculitis
Necrotising, granulomatous inflammation in upper and lower respiratory tract
= pulmonary Hg & fibrosis
*assoc/ w/ proliferative, crescentic glomerulonephritis
Ix
serum C-ANCA (anti-neutrophil cytoplasmic antibody)
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